Nā kumu a me ke ʻano o ka hoʻomohala ʻana o ka ketonuria

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Hāʻawi kēia hana i kahi maʻi ka hopena o kekahi ʻano ʻē aʻe - ka hiki ʻana o kahi moku ketonemia (aka acetonemia) - ke ʻano o ke koko o nā acetone (ketone) pūpuna.

Ma muli o ka filtration o ke koko e nā keiki, hiki i ka acetone ke komo i ka urine, ʻoi aku ka maʻalahi o ka ʻike i loko o ka laboratorium ma mua o ke koko.

Hāʻawi kēia i ke kumu e manaʻo ai i ka noho ʻana o ka maʻi maʻi a me nā kūlana ʻē aʻe kahi e hoʻokaʻawale ʻia ai kēia ʻano mea kanu maʻalahi i kahi wahi iʻike ʻole ʻia ai kona ʻike.

He aha ka ketonuria?

ʻO ka Acetone kahi mea hana ikaika a mau loa ia, ma muli o nā hiʻohiʻona hiʻohiʻona o kāna molekane, ʻaʻole wale ia i hiki ke hoʻopilikia i ka wā o kahi hopena kūlohelohe.

A ʻo nā hopena like ʻole e hoʻokela i ka hana a ka wā e hana ai i nā hana ʻehā (hoʻoheheʻe ʻia i ka pāpaʻu palupalu), e hana ai i ka hopohopo kūpono i ka wā e loaʻa ai nā kaʻina kūloko i loko o ke kino. Me ka maʻalahi o ka mea e hoʻokiʻoki i ka acetone i kahi palaʻa mai ka lole, hoʻowalewale ʻia ia i nā lipids i nā mea laʻa o ke kino, ʻaʻole makemake i kona manaʻo e pili ana i kēia kumuhana, a hiki no hoʻi ke hana i nā pilikia like ʻole.

Ma kahi kino kino olakino, hiki ke hōʻike ʻia ka nui o ka acetone i ke koko e ka huaʻōlelo: ka hiki ʻana o nā ʻāpana o ka waiwai, no ke koko he 1-2 mg / 100 ml, no ka urine - ʻaʻole iʻoi aku ma mua o ka 0,01-0.03 g i ka nui o ka lā. Ma kahi kīnā ʻole, ʻaʻole i lohi kēia mau mea i ka manawa lōʻihi i ka mea i loko o ka mana o ke koko a i ʻole kaomi paha, e neʻe aku me ia, a i ʻole ka pelu, a me ka ea i hoʻoneʻe ʻia e ka ʻōpū.

Eia nō naʻe, i kekahi mau kūlana, ʻaʻole mākou i kamaʻilio e pili ana i nā ʻāpana o kahi mea i loko o ke kino, akā e pili ana i ka hopena ʻona i luna, no ka mea ua pae kona pae ma ke koko a me nā kikoʻī i loko o ka urine hoʻonui nui (alakaʻi i ka hanana ʻana o nā hanana o ketonemia a me ketonuria).

Nā kumu a me nā hōʻailona o ke alualu

ʻO Ketonuria, waiwai ʻole a hōʻino ʻole ʻia i ke kino, hiki ke hopena i nā kumu kūlohelohe:

  • keu me ka wai momona, ka meaʻai me ka nui o ka paʻakikī e wāwahi i nā protein a me nā momona, akā me ka hapa ʻole o nā hāmeʻe;
  • inu waiʻona.

No ka mea, ʻo nā kino ketone i loko o ke koko (ma ka manawa o ka acetone, acetoacetic a me acids-hydroxybutyric acid) i hopena o nā kaʻina hana e hana nei i loko o ka ate (glycogen breakdown), kā lākou hōʻemi i ke koko a me ka nui i loko o ka urine ma muli o kāna hana.

ʻO nā kumu ʻē aʻe (ma ke ʻano o ka nui o ka noi no ka glycogen) e pili i nā koho a pau no ka wikiwiki a i nā kūlana paha:

  • ka pōloli ma ka nele o ka maikaʻi o ka meaʻai (a i ʻole ka manaʻa) i ʻole o ka ʻai, a i ʻole ka mea i aloha ʻia ʻole, a i ʻole kekahi wahi i loko o ka ʻōnaehana kaiʻai (ma waena o nā mea helehelena, bodybuilders, nā mea mālama i kēlā me kēia ʻano ʻoihana);
  • ka mānoina ma muli o kahi kaʻina oncological (ʻoi pūpū o ka ʻōpū), ʻo ke ala o kahi maʻi ʻeha;
  • luhi ma muli o ka hana kino koʻikoʻi, maʻi hypothermia;
  • ka nalowale o nā mea ʻai i ka hihia o ke kipi ʻana o ke kaʻina hana i loko o ka ʻawaʻawa, a me ke keʻe ʻana i ka ʻōpū a me nā stenosis o kāna pylorus a i esophagus;
  • ma muli o ka hoʻohālikelike pinepine a i ʻole mauʻuʻi (indomitable ka luaʻi i loko o kahi wahine hāpai a me ka eclampsia i ka wā o ka maʻi pakanika hope loa), ʻeha.

ʻO nā hihia o ka anemia a me nā maʻi mellitus e hāʻule i ka māhele like. I ka hihia mua, ʻaʻole lawa nā nui o nā kelua lawe i nā ʻōpū o nā huaʻai, ma ka lua - ke kū ʻole o ka pae kūwaho o ka glucose e hoʻoneʻe ana i ka neʻe mai ka glycogen depot i loko o ka ate.

ʻO kahi ʻano ketonuria paha he hōʻailona paha:

  • nā pōʻino kaumaha (alakaʻi, phosphoric, atropine intoxication);
  • mahana lōʻihi;
  • manawa noho o ke kaʻina hana ma hope o ka hoʻomaʻamaʻa (inā paha ma hope o anesthesia chloroform).

ʻO ke kūlana o ka ketonuria ma muli o ka nui o ka pono o nā mea kākoi a me kahi kiʻekiʻe o kā lākou ʻai, ʻike ʻia me ka thyrotoxicosis a me nā kūlana me ka nui o ka excitability a me ka huhū o ka nenoai sentral:

  • hemorrhages o ka'āina subarachnoid;
  • nā hōʻeha poʻo;
  • moku'āina precomatous.

ʻO ka hōʻeha ʻana o nā maʻi aʻalolo e like me ka maʻiʻulaʻula, ka maʻi a me ka hele ʻana o nā mea i ʻoi aku ka maʻi (tuberkulosis, meningitis) e alakaʻi ana i ka acetonuria, akā ʻaʻole ia he hoʻokolohua diagnostic i loko o kēia mau hihia.

ʻO Ketonuria i ka mellitus maʻi mellitus kūpono loa i ka nānā - e hōʻike ana i kona neʻe i kahi hōʻeha o ka maʻi a i ʻole ke ala o nā kūlana hou aʻe o ka maʻi (acetone crisis a hyperglycemic coma).

Me kēia mau mea, ʻo ka hiki ʻana o ka acetonuria hoʻokaʻawale (me ke kūlike o ka glucosuria - ka nalowale o ka glucose i ka urine) hiki iā ʻoe ke pale malū aku i ka maʻi diabetes mai ka papa inoa o nā kumu i kumu ʻia ai.

ʻO kekahi kumu i ke ketonuria ʻo ka loaʻa ʻana o nā hyperinsulinism e loaʻa ana a me ka congenital (a i ʻole ka hypoglycemic maʻi) - kahi ʻano nui o ka nui o ka insulin i loko o ke koko me ka hāʻule o ka glucose ʻaʻole i hoʻokumu ʻia e ka maʻi mellitus.

ʻO nā ʻōmaʻomaʻo o ka ketonuria ka mea aʻona o ka acetone koi i loko o nā mea huna o ke kanaka.

Hiki iā ia:

  • ea i ka ea;
  • hiō
  • heokeo.

ʻO nā hōʻailona hoʻohālike i ka pākeke he lethargy, mental kaumaha, apathy.

I nā keiki, ʻo ia ka:

  • hōʻole ʻaʻole wale mai ka meaʻai, akā mai ka wai hoʻi (ma muli o ke kaila mau);
  • nā hōʻailona o ka maloʻo (hōʻea, lethargy, nāwaliwali i ka ʻili maloʻo a me ka alelo);
  • ke ka okana ana o ka psyche, i hoohuoi ia e kona hooluhi;
  • nā hōʻike kikoʻī i loko o ka ʻōpū (ma ka maʻamau ʻo ka umbilical region);
  • ninini
  • paikini hele ana me ka inu ana a me ka ai ole;
  • ke ala ʻana o ke ea kino ma kahi hope o ke kino o ka ʻili me kahi ʻulaʻula ʻole i ka maka;
  • hāpū hina acetone, ʻūpū a me ka hoʻopuʻi pahū.

I nā wahine hāpai, ʻo ka hele a me ka ulu ʻana o kēia mau hōʻailona (me kaʻai nui a me ka hana kino kūpono) e hōʻike nei:

  • ka hoʻomohala ʻana o ka maʻi toxicosis;
  • maʻi ʻana o ke kino;
  • nā pilikia paʻakikī;
  • hapai maʻi.

Video ma ke maʻi maʻi maʻi:

Ma muli o nā hopena olakino e pili ana i ka pūpū, ketonemia a me ka ketonuria e pono e noʻonoʻo pono a me nā kūpono kūpono no ka hoʻokele a me ka mālama ʻana i ka maʻi (a ʻo ka mea mua loa, ka hoʻihoʻi ʻana o ka hoʻokaʻina wai).

Ma muli o ka ʻike nui o ka mālama glycogen i loko o ka puʻuwai o ke keiki, hele koke ko lākou poʻomanaʻo, e alakaʻi ana i nā ʻōpū pololi me ka pono o ka hōʻemi ʻana i nā momona ʻē aʻe.

ʻO ka hemahema a i ʻole hōʻino ʻia o kā lākou oxidation e hoʻokūkū ai i ka acetonemia me ka hanana ʻana o ka mauʻu acetoemic a me kahi mea ʻala kikoʻī o kahi mea i hāʻawi ʻia mai ka luaʻi.

Hoʻopili i kahi pilikia o ka loaʻaʻana o nā protein a me nā momona (inā i loaʻa ka nui i ka meaʻai), hiki i kona helehelena ke hopena i ka hyper-excitability o ke keiki, hiki ke hoʻohuli hou i loko o kahi kūlana acetone pilikia.

ʻO nā ʻōmua mua ma mua:

  • hiamoe
  • makehewa;
  • wela (piʻi i ke kauwela);
  • colic i loko o ka ʻōpū.

ʻO ka maʻamau maʻamau o ka hīmeni acetonemic e hui pū me ka acetonuria e koi i kahi mea ʻē aʻe:

  • diabetes mellitus;
  • hopena kino;
  • nā maʻi tumio;
  • kalawai o ka pūpū.

ʻO nā kumu ʻē aʻe o ka acetonuria wā kamaliʻi:

  • kōkuhi piha ka holomaka;
  • ka hele ʻana ma nā meaʻai o nā ʻāpana he nui o nā preservatives, nā ʻohu, nā mea hoʻonaninani o ka hua ʻana o ka kemika, a me nā ʻikena e lawe ʻia a i ʻole;
  • kiʻekiʻe ke olakino a noʻonoʻo kino;
  • ka hanela helminthic, diathesis (hoʻohaʻahaʻa i ka pae o ke kūlohelohe kūlohelohe);
  • ola ke kūlana koʻikoʻi, hyperthermia, hypothermia.

ʻO ke kumu no ke ketonuria o nā pēpē hou e hoʻomaʻamaʻa ana a i ʻole ke ola ʻana o kona ʻano nui, ke hoʻololi ʻana i ka genetically - leucinosis, kahi mea i loaʻa i loko o 30 mau keiki a (no ka maʻi hōʻeha o ka ʻōnaehana ma waena o ka ʻōnaehana) e pau i ka make.

Hiki ke maʻalahi ka hoʻomāliʻiliʻi o ka ketonuria e ka hoʻohana ʻana o ka hana diagnostic wikiwiki - paʻa ka waiola i ka wā e hoʻohana ai i nā kānana hoʻokolohua (ma ʻekolu mau manawa a hoʻokahi) a me ka ʻōmole me ka hopena ammonia - inā hoʻohui ʻia i ka urine i loaʻa nā kino ketone, e ʻulaʻula kona ʻulaʻula.

Nā wikiō mai Dr. Komarovsky:

Nā lāʻau lapaʻau

Ma muli o ke ʻano o ka paʻakikī o nā maʻi paʻakikī ma muli o ka acetonuria, pono e alakaʻi ʻia ka mea maʻi i ka mea ʻike e hoʻopili aku ai.

Ma mua o ka makewai mau ʻana a me ka pōloli, wikiwiki a me ka nui o ka urination, ke kaumaha kaumaha, a me nā hōʻailona o ka hoʻohemo, pono pono e ʻimi i ka endocrinologist, ʻo ka hele ʻana o ke kuni a me nā hōʻailona o ka maʻi e koi ai ka manaʻo o ka mea maʻi loea.

ʻO kahi mea inu waiʻona i ukali ʻia e ka acetonuria he kumu e hoʻopili ai i ka lāʻau n narologist, aʻo ka hana mua me ka anesthesia ke kuleana o ka resuscitator. ʻO nā hōʻailona o ka hyperinsulinism a i ʻole thyrotoxicosis e lilo i kumu no ka hoʻokolokolo ʻana e kekahi endocrinologist.

Pono nā wahine hāpai ʻia e kipa aku i kahi obstetrician-gynecologist, nā makuahine me nā keiki maʻi - kahi maʻi maʻi. ʻO nā hōʻeha ʻo ke poʻo me nā maʻi cerebral a i ʻole nā ​​mea make a ke ala hiki i ke keʻena o kahi neurologist a i mea maʻi laʻa, inā ua manaʻo ʻoe he neoplasm malignant, pono ʻoe e hoʻokaʻa i kahi oncologist, a inā ʻaʻole maopopo ka haukapila, e nīnau aku i kahi mea lapaʻau.

Ma muli o nā hōʻailona i hōʻike ʻia, kuhikuhi ke kauka i ka hoʻokolohua e kuhikuhi i nā hoʻokolohua pono a me ka hōʻike hoʻokolohua. ʻO ka nui o ka ʻikepili i loaʻa i ke kumu o ke koho pono ʻana o ke kūlana kūpono e pono ai.

Hiki i ka nui o nā ala lapaʻau ke komo pū me ka hoʻoponopono ʻana o ka hiamoe, hoʻomaha a me ka mea ʻai, a me nā hana hōʻiliʻili paʻakikī i ke kumu oncological o ke ʻano. I loko o ka maʻi diabetes genesis o acetonuria, ua kuhikuhi ʻia ka lāʻau e ka endocrinologist me ka noʻonoʻo ʻana i ke ʻano o ka pathology concomitant (ate, gastrointestinal upets, etc.). Pono ka mea maʻi e kū pinepine no kahi hōʻike hoʻāʻo e loiloi i ka hopena o ka hana.

ʻO kahi kiʻekiʻe kiʻekiʻe o ka ketonuria kahi hōʻailona no ka mālama maʻi.

No ka hoʻohui i nā wai, he mea kūpono e hoʻohana i nā hopena o nā Orsol a i Regidron, a i ʻole kahi decoction raisins, nā hua ʻē aʻe, ka wai alkaline me ka ʻole o ka hau.

Inā hiki ʻole ke inu ma ka luaʻi, mālama ʻia ka wai i ka makua (intravenously drip), ʻo ka ʻae o Cerucal e ʻae ai i ka wehe ʻana i ka luaʻi.

Loaʻa ka pahuhopu i ka wehe ʻana i nā toxins ma ka hoʻohana ʻana i nā sorbents (Sorbeks, carbon carbon activated), e kau ana i ka enema hoʻomaʻemaʻe (me ka concomitant hyperthermia, e hoʻohui i ka 1 tbsp. ʻO ka paʻakai i kēlā me kēia lita o ka wai).

Hoʻoulu ʻia ka meaʻai e ka mea ʻai kaiʻai loea.

ʻO ka ʻiʻo (turkey, kuniti, pipi) i ʻai ʻia i ka ʻū a ʻai ʻia. Ma ke ʻano he papa mua, makemake mākou i ka borsch, ka mea kanu meaʻai, i ka puna, a me ka iʻa momona haʻahaʻa.

Me ke ala o ka rehydration a me ka hoʻonui hou i nā mea trace a me nā huaora, nā wai a me nā wai ʻona, hoʻopili ʻia (compice quince compote).

Hōʻole loa ia e hoʻohana:

  • kahalaha;
  • momona (ʻoiai ma ke ʻano o kahi hāmona);
  • nā mea ʻala;
  • nā huaʻomoʻa citrus;
  • maiʻa.

No ka mea e pono e hoʻokaʻawale ʻia kahi ʻokoʻa ma waena o nā kumu o ka acetonuria - i ka wī i makemake ʻia ke kumu no ka ikaika o ka lolo a me nā ʻano āpau o ka kiko o ke kino.

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